[Melanotic progonoma in an infant. Apropos of a case]

The authors report one observation of a melanotic progonoma or melanotic neuroectodermal tumor of the infant. They remind the etiologic and pathogenic data of this rare affection. They insist on the neuroectodermal pathogenesis with embryologic, histologic, ultrastructural and histoenzymologic bases. The maxillary location is encountered in 70% of the cases, it is facial cervical in 90% of the cases. The evolution is considered as benign with chirurgical management but the review of the literature shows 6 definite malignant cases, therefore the malignancy would be 3.5%.