Apical hypertrophic cardiomyopathy with left ventricular apical aneurysm: Importance of multi-modality imaging

Nisharahmed Kherada1, Juan M Vinardell2, Christos G Mihos3

  • 1Columbia University Division of Cardiology at the Mount Sinai Heart Institute, Miami Beach, FL, USA.

Insights

Apical hypertrophic cardiomyopathy (HCM) with left ventricular apical aneurysm is rare. Multimodality imaging aids in identifying this condition for better risk assessment and treatment planning.

Area of Science:

  • Cardiology
  • Medical Imaging

Background:

  • Apical hypertrophic cardiomyopathy (HCM) is a rare variant of HCM, distinct from the more common septal hypertrophy.
  • A left ventricular apical aneurysm occurs in 2% of HCM patients, significantly raising the risk of sudden death.

Observation:

  • This case highlights apical HCM with a coexisting left ventricular apical aneurysm.
  • The diagnosis was established using a combination of imaging modalities.

Findings:

  • Multimodality imaging, including ECG, echocardiography, ventriculography, and cardiac MRI, is crucial for accurate diagnosis.
  • This approach allows for precise identification of the specific morphologic pattern of apical HCM with aneurysm.

Implications:

  • Accurate diagnosis through multimodality imaging is essential for appropriate risk stratification in patients with apical HCM and aneurysm.
  • Effective treatment planning relies on the comprehensive information provided by these imaging techniques.

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