Successful Surgical Treatment of an Aggressive Pelvic Angiomyxoma With Intracardiac Extension

Annastiina Husso1, Jukka Savola1, Jarmo Gunn2

  • 1Department of Cardiothoracic Surgery, Heart Center, Turku University Hospital, Turku, Finland.

Insights

A rare pelvic angiomyxoma invaded the heart, posing significant surgical risks. Successful complex resection on cardiopulmonary bypass allowed for patient recovery and subsequent hormonal therapy.

Area of Science:

  • Cardiovascular Surgery
  • Gynecologic Oncology
  • Vascular Surgery

Background:

  • Pelvic angiomyxoma is a rare benign tumor with a propensity for local invasion.
  • Intracardiac extension of pelvic tumors is exceptionally uncommon and presents significant management challenges.
  • The initial presentation mimicked caval and intracardiac thrombus, delaying definitive diagnosis.

Observation:

  • A case is presented of a patient with a pelvic angiomyxoma extending into the right atrium and right ventricle.
  • The tumor involved the suprarenal vena cava and left iliac vein.
  • Surgical intervention was deemed high-risk due to the extensive tumor infiltration.

Findings:

  • The tumor was successfully resected from the right atrium, suprarenal vena cava, and left iliac vein.
  • The procedure required cardiopulmonary bypass and deep hypothermic circulatory arrest.
  • Affected gynecological organs were removed concurrently.

Implications:

  • This case highlights the importance of thorough investigation for rare pelvic tumors with unusual extensions.
  • Complex surgical techniques, including cardiopulmonary bypass, can be safely employed for extensive tumor resections.
  • Multidisciplinary management is crucial for optimizing outcomes in rare oncologic and vascular cases.

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