Congenital chylous ascites in infants: another presentation of intestinal malrotation

Li Long1, Chen Zhen1, Wei Yandong2

  • 1Department of Pediatric Surgery, Capital Institute of Pediatrics-Peking University Teaching Hospital, Beijing, 100021, People's Republic of China; Medical Department, Peking University, Beijing, 100000, People's Republic of China.

Insights

Intestinal malrotation can cause congenital chylous ascites in infants. Ladd

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Neonatal Medicine

Background:

  • Congenital chylous ascites in infants often has an unclear etiology.
  • Intestinal malrotation is increasingly recognized as a potential cause.

Purpose of the Study:

  • To investigate intestinal malrotation as a cause of congenital chylous ascites in infants.
  • To report on the clinical experience and treatment outcomes.

Main Methods:

  • Retrospective analysis of 10 infants with chylous ascites (2001-2014).
  • Preoperative conservative management was initiated for all patients.
  • Surgical intervention, including Ladd's procedure, was performed for malrotation.

Main Results:

  • Nine of ten patients had intestinal malrotation.
  • Ladd's procedure (laparoscopic or open) was performed in nine patients.
  • All patients achieved resolution of chylous ascites post-surgery with no significant recurrence.

Conclusions:

  • Intestinal malrotation can obstruct lymphatic flow, leading to congenital chylous ascites.
  • Ladd's procedure is a safe and effective treatment for infantile chylous ascites caused by malrotation.
Abstract

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