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The relationship between dietary intake, growth and body composition in Phenylketonuria

Maureen Evans1, Helen Truby2, Avihu Boneh3

  • 1Department of Metabolic Medicine, The Royal Children's Hospital, Flemington Road, Parkville, Melbourne, Victoria 3052, Australia; Department of Nutrition and Food Services, Royal Children's Hospital, Flemington Road, Parkville, Melbourne, Victoria 3052, Australia; Be Active Sleep Eat (BASE) Facility, Department of Nutrition and Dietetics, Monash University, Faculty of Medicine, Nursing and Health Sciences, Level 1, 264 Ferntree Gully Road Notting Hill, Melbourne, Victoria 3168, Australia.

Molecular Genetics and Metabolism
|July 26, 2017
PubMed
Abstract

Keywords:
Body compositionGrowthPhenylalanine restricted dietPhenylketonuriaProtein:Energy ratio (P:E ratio)

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