Biventricular Repair in Interrupted Aortic Arch Type C With Aortic Atresia

Area of Science:

• Cardiology
• Pediatric Cardiac Surgery
• Congenital Heart Disease

Background:

• Interrupted aortic arch type C with aortic atresia is a rare and severe congenital heart defect.
• Ventricular septal defects often accompany interrupted aortic arch, complicating surgical repair.
• Single-stage biventricular repair aims to correct complex heart anomalies in one procedure.

Observation:

• A case involving interrupted aortic arch type C, aortic atresia, and a ventricular septal defect in a patient with two well-developed ventricles.
• The patient underwent a single-stage biventricular repair utilizing the modified Yasui procedure and aortic arch reconstruction.

Findings:

• Successful single-stage biventricular repair with modified Yasui procedure and arch reconstruction was performed.
• Postoperative angiography revealed bilateral brachiocephalic trunks with high branching.
• The patient demonstrated positive long-term outcomes, remaining well six years after the operation.

Implications:

• The modified Yasui procedure is a viable and effective surgical option for complex interrupted aortic arch with aortic atresia.
• Single-stage repair strategies can lead to favorable long-term results in pediatric patients with severe congenital heart defects.
• This case highlights the importance of innovative surgical techniques in managing complex congenital heart disease.