Role of cardiac pacing in congenital complete heart block
Stephanie F Chandler1,2, Francis Fynn-Thompson3,4, Douglas Y Mah1,2
1a Department of Cardiology , Boston Children's Hospital , Boston , MA , USA.
Insights
Congenital complete heart block often requires pacemaker implantation in children. This review examines patient and technical factors for optimal pacing strategies and long-term outcomes.
Area of Science:
- Pediatric Cardiology
- Electrophysiology
- Congenital Heart Disease
Background:
- Congenital complete heart block affects 1 in 15,000 infants, often due to maternal antibodies.
- Most affected children require pacemaker implantation before adulthood.
- Systemic lupus erythematosus and Sjogren's syndrome are common maternal causes.
Purpose of the Study:
- To review patient and technical factors influencing pacemaker selection in congenital complete heart block.
- To evaluate current literature on optimal pacing practices for pediatric patients.
- To discuss alternative pacing strategies and long-term complications.
Main Methods:
- Literature search conducted using PubMed, Embase, and Web of Science.
- Review of data on epicardial versus transvenous implants.
- Analysis of pacing-induced ventricular dysfunction and alternative pacing techniques.
Main Results:
- Various pacing strategies exist for pediatric congenital complete heart block.
- Risks and benefits of initial pacemaker implant require careful consideration.
- Long-term implications of lifelong pacing are a critical factor.
Conclusions:
- Numerous pacing strategies are available for children with congenital complete heart block.
- Balancing initial implant risks with long-term pacing issues is essential.
- Optimal pacing practices require individualized patient and technical assessment.
Introduction:
Congenital complete heart block affects 1/15,000 live-born infants, predominantly due to atrioventricular nodal injury from maternal antibodies of mothers with systemic lupus erythermatosus or Sjogren's syndrome. The majority of these children will need a pacemaker implanted prior to becoming young adults. This article will review the various patient and technical factors that influence the type of pacemaker implanted, and the current literature on optimal pacing practices. Areas covered: A literature search was performed using PubMed, Embase and Web of Science. Data regarding epicardial versus transvenous implants, pacing-induced ventricular dysfunction, alternative pacing strategies (including biventricular pacing, left ventricular pacing, and His bundle pacing), and complications with pacemakers in the pediatric population were reviewed. Expert commentary: There are numerous pacing strategies available to children with congenital complete heart block. The risks and benefits of the initial implant should be weighed against the long-term issues inherent with a life-time of pacing.
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