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Published on: July 18, 2014
Endocarditis of a congenital coronary fistula in a child
Thomas Krasemann1, Ingrid M van Beynum1, Ingrid M E Frohn-Mulder1
1Sophia Kinderziekenhuis,Department of Pediatric Cardiology,Erasmus Medical Centre Rotterdam,Rotterdam,The Netherlands.
Insights
Congenital coronary fistulas are rare in children. This case highlights endocarditis in a 9-year-old boy with a right coronary artery fistula, successfully treated with antibiotics and interventional closure.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Interventional Cardiology
Background:
- Congenital coronary artery fistulas (CCAFs) are rare vascular anomalies.
- Endocarditis complicating CCAFs is exceptionally uncommon, particularly in pediatric patients.
- This case presents a unique instance of CCAFs in a child.
Observation:
- A 9-year-old boy presented with a fistula originating from a dilated right coronary artery.
- The fistula connected the coronary artery to the junction of the superior vena cava and right atrium.
- The patient developed infective endocarditis, a rare complication of this anomaly.
Findings:
- The patient received a 6-week course of antibiotics to manage the endocarditis.
- Interventional closure of the coronary fistula was performed 3 months after initial treatment.
- An Amplatzer vascular plug was successfully used for the fistula closure.
Implications:
- This case underscores the importance of considering endocarditis in pediatric patients with CCAFs.
- Successful interventional closure demonstrates a viable treatment option for complex CCAFs.
- Early diagnosis and management are crucial for favorable outcomes in pediatric patients with CCAFs.
Abstract:
Endocarditis of congenital coronary fistulas in the cardiac chambers is rare, especially in the paediatric age group. We describe the case of a 9-year-old boy with a fistula from the dilated right coronary artery to the junction of the superior caval vein to the right atrium, complicated by endocarditis. Treatment consisted of 6 weeks of antibiotics and interventional closure of the fistula 3 months later with an Amplatzer vascular plug.
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