Intestinal obstruction due to kaposiform hemangioendothelioma in a 1-month-old infant: A case report

Joong Kee Youn1, Shin-Hoo Park, Ji-Won Han

  • 1Department of Pediatric Surgery, Seoul National University College of Medicine, Seoul, Korea.

Medicine
|September 15, 2017
PubMed

Insights

Kaposiform hemangioendothelioma (KHE) in the intestine is rare but can cause obstruction. Complete surgical resection offers a successful treatment for this aggressive vascular tumor in infants.

Area of Science:

  • Pediatric Oncology
  • Vascular Malformations
  • Surgical Gastroenterology

Background:

  • Kaposiform hemangioendothelioma (KHE) is an aggressive vascular tumor typically affecting infants and children.
  • While cutaneous and visceral forms are more common, intestinal KHE is a rarer presentation.
  • Intestinal KHE has a better prognosis if localized and without coagulopathy, but data remains limited.

Observation:

  • A 1-month-old female infant presented with abdominal distention and bilious vomiting.
  • Diagnostic workup suggested intestinal obstruction.
  • Surgical exploration revealed a jejunal mass causing obstruction.

Findings:

  • The infant underwent successful small bowel segmental resection and anastomosis.
  • Pathological examination confirmed the mass as intestinal type Kaposiform Hemangioendothelioma.
  • The patient was discharged symptom-free post-surgery.

Implications:

  • Intestinal KHE can manifest as a critical cause of bowel obstruction in infants.
  • Complete surgical resection is a viable and effective management strategy.
  • Further case reporting and research are crucial for understanding treatment options and prognosis for intestinal KHE.
Abstract

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