Congenital left atrial appendage aneurysm: Atypical presentation
Mehdi Bamous1, Mahdi Aithoussa1, Ayoub Abetti1
1Department of Cardiovascular, Cardiac Surgery Unit, Mohamed V Military Hospital, Mohammed V University, Rabat, Morocco.
Annals of Pediatric Cardiology
|September 21, 2017
Summary
Congenital left atrial appendage aneurysm, a rare condition from atrial muscle dysplasia, was surgically resected in a 14-year-old boy presenting with atypical cough symptoms. This case highlights the importance of considering rare cardiac anomalies in pediatric patients.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Congenital left atrial appendage aneurysm is a rare condition.
- It results from congenital dysplasia of the atrial muscles.
Observation:
- A 14-year-old boy presented with a 5-month history of cough.
- The patient was in sinus rhythm.
- Transthoracic echocardiography and computerized tomographic angiography confirmed the aneurysm of the left atrial appendage.
Findings:
- Surgical resection of the left atrial appendage aneurysm was performed via median sternotomy on cardiopulmonary bypass.
- The patient's atypical clinical presentation included a persistent cough.
Implications:
- This case underscores the rarity of congenital left atrial appendage aneurysm.
- It emphasizes the need for considering uncommon cardiac pathologies in pediatric differential diagnoses.
- The atypical presentation highlights the variability in clinical manifestations of this rare condition.
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