Related Experiment Videos
Inflammatory myofibroblastic lung tumor with dysphagia in a 4-year-old child
Vinitha V Nair1, Kunal Krishna Singh1, Joseph Thomas Kathayanat1
1Department of Cardiovascular and Thoracic Surgery, 29319 Government Medical College , Kottayam, Kerala, India.
Insights
Inflammatory myofibroblastic tumors are rare in adults but can occur in children. This case highlights a rare presentation of dysphagia in a pediatric patient with a lung mass, successfully treated with surgery.
Area of Science:
- Pediatric Oncology
- Thoracic Surgery
- Pathology
Background:
- Inflammatory myofibroblastic tumors (IMTs) are uncommon neoplasms with a variable presentation.
- While rare in adults, IMTs are a significant cause of pediatric lung tumors.
- Dysphagia is an exceptionally rare presenting symptom for pulmonary IMTs.
Abstract:
Inflammatory myofibroblastic tumors of the lung are rare in adults but common among pediatric lung tumors. A 4-year-old girl was evaluated for respiratory symptoms, dysphagia, and weight loss. Radiology revealed a right hilar mass that persisted despite antibiotic treatment. On exploration, a hilar mass involving the pulmonary vasculature, diaphragm and gastroesophageal junction was found. Aggressive surgical excision including a right pneumonectomy was performed. Histopathology confirmed an inflammatory myofibroblastic tumor with no features of malignancy. At the 2-year follow-up, the child was clinically stable with no recurrence. Dysphagia is a very rare presentation of such tumors.