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Maxillofacial Mazabraud's syndrome: A case report & review
S Domancic1, N Pezoa2, M Fernandez-Toro3
1Universidad de Chile's Bucco-Maxillofacial Surgery and Traumatology Department, Sergio Roberto Livingstone Polhammer 943, Independencia, Metropolitan Region, Chile.
Journal of Stomatology, Oral and Maxillofacial Surgery
|October 15, 2017
Summary
Mazabraud's syndrome, a rare condition linking intramuscular myxoma and fibrous dysplasia, presents a diagnostic challenge, especially in the head and neck. This case highlights its rarity and the need for better treatment guidelines.
Area of Science:
- Endocrinology
- Oncology
- Pathology
Background:
- Mazabraud's syndrome is a rare disorder characterized by the coexistence of intramuscular myxomas and fibrous dysplasia.
- While around 80 cases are documented, its occurrence in the head and neck region, particularly involving the mandible, is exceptionally uncommon.
Observation:
- A unique case of Mazabraud's syndrome is presented in a 63-year-old female.
- The patient exhibited fibrous dysplasia of the mandible alongside a soft tissue myxoma in the edentulous alveolar ridge of the molar region.
Findings:
- The report details the clinical, imaging, and microscopic findings crucial for diagnosing this rare condition.
- A four-year follow-up provides insights into the disease's progression and management.
Implications:
- This case underscores the diagnostic and therapeutic complexities associated with Mazabraud's syndrome.
- Further understanding of its behavior is essential for developing effective treatment protocols and clinical guidelines.
