True congenital atresia of the left main coronary ostium: delayed presentation
Varadaraju Raju1, Ramesh Chandrashekar Hebbale1, Chandra Sena Muniswamy1
11 Department of Cardiothoracic and Vascular Surgery, 29164 Sri Jayadeva Institute of Cardiovascular Sciences and Research , Bangalore, Karnataka, India.
Insights
Congenital atresia of the left main coronary ostium, a rare heart defect, can cause adult unstable angina. Surgical bypass using arterial grafts effectively treated this rare coronary anomaly.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Coronary Artery Anomalies
Background:
- Congenital atresia of the left main coronary ostium is an extremely rare coronary artery anomaly.
- This condition typically presents in adulthood with symptoms of coronary artery disease, such as unstable angina.
Observation:
- A 48-year-old male presented with symptoms of unstable angina.
- Coronary angiography revealed an absent left main coronary ostium.
- A super-dominant right coronary artery was observed retrogradely filling the left coronary system.
Findings:
- Computed tomography-angiography with 3-dimensional reconstruction confirmed the congenital absence of the left main coronary artery.
- The patient underwent total arterial revascularization due to persistent chest pain.
- A left internal mammary artery-left radial artery Y-graft was utilized for the bypass surgery.
Implications:
- This case highlights the importance of considering rare coronary anomalies in the differential diagnosis of adult-onset coronary artery disease.
- Surgical revascularization, particularly total arterial grafting, can be a successful treatment strategy for congenital atresia of the left main coronary ostium.
- Further research into the long-term outcomes of surgical management for this rare anomaly is warranted.
Abstract:
Congenital atresia of the left main coronary ostium is a rare coronary anomaly presenting in adulthood. A 48-year-old man presented with unstable angina. Coronary angiography showed an absent left coronary ostium with a super-dominant right coronary artery retrogradely filling the left system. Computed tomography-angiography with 3-dimensional reconstruction confirmed the absence of the left main coronary artery. In view of ongoing chest pain, the patient was offered coronary artery bypass surgery. Total arterial revascularization was performed with a left internal mammary artery-left radial artery Y-graft.
More Related Videos
Related Concept Videos
Mitral Stenosis I: Introduction
Mitral Stenosis II: Clinical features and Diagnostic Tests
Coronary Circulation
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Cardiac Catheterization III: Left Heart Catheterization
Mitral Valve Prolapse I: Introduction
Coronary Artery Disease III: Clinical Manifestations


