Huntington disease care: From the past to the present, to the future

T A Mestre1, K Shannon2

  • 1Parkinson's Disease and Movement Disorders Center, Division of Neurology, Department of Medicine, The Ottawa Hospital Research Institute, University of Ottawa Brain and Mind Institute, Ottawa, Canada.

Insights

Multispecialty care is recommended for Huntington disease (HD) management, but more research is needed. Technology integration in multispecialty care shows potential for easing patient and caregiver burdens.

Area of Science:

  • Neuroscience
  • Neurology
  • Genetics

Background:

  • Huntington disease (HD) is a progressive neurodegenerative disorder with no cure.
  • The complex clinical presentation of HD necessitates comprehensive patient management.
  • Progressive loss of independence and increasing disability complicate HD care.

Purpose of the Study:

  • To review current literature and expert opinions on Huntington disease care.
  • To highlight the importance of multispecialty and palliative care in HD management.
  • To explore the potential of technology in improving HD care delivery.

Main Methods:

  • A literature review was conducted.
  • An expert-based statement was formulated.

Main Results:

  • Symptomatic treatment for chorea is the only current indication.
  • Multispecialty care involving physicians, therapists, social workers, and nutritionists is crucial.
  • Palliative care improves quality of life and may delay nursing home placement.
  • The optimal care delivery model for HD remains undetermined.

Conclusions:

  • Evidence supports multispecialty care for HD, but further clinical research is required.
  • Integrating technology into multispecialty care can reduce burdens on families and healthcare teams.
  • Technological advancements offer potential for broader and more effective HD care delivery.
Abstract

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