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Updated: Feb 19, 2026

Generation of Human Nasal Epithelial Cell Spheroids for Individualized Cystic Fibrosis Transmembrane Conductance Regulator Study
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Lung function decline is delayed but not decreased in patients with cystic fibrosis and the R117H gene mutation

Jeffrey S Wagener1, Stefanie J Millar2, Nicole Mayer-Hamblett3

  • 1Department of Pediatrics, University of Colorado, Aurora, CO, USA.

Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society
|November 5, 2017
PubMed
Abstract

Keywords:
Cystic fibrosisF508delLung functionLung function declineR117H

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