PARACENTRAL ACUTE MIDDLE MACULOPATHY IN PRIMARY CONGENITAL GLAUCOMA

Area of Science:

• Ophthalmology
• Medical Case Reports

Background:

• Primary congenital glaucoma (PCG) is a rare developmental disorder affecting infants.
• Paracentral acute middle maculopathy (PAMC) is an ischemic condition affecting the macula.

Observation:

• A 14-year-old female presented with sudden vision loss.
• Ophthalmic examination revealed signs of PCG including Haab striae and optic disc hemorrhages.
• Fundoscopy showed a fern-like white macula lesion.

Findings:

• Optical coherence tomography (OCT) demonstrated hyperreflective plaques in the inner nuclear/outer plexiform layers.
• OCT angiography revealed ischemia in the deep capillary plexuses.
• These OCT findings were consistent with PAMC.

Implications:

• This is the first reported case linking PCG and PAMC.
• PCG may be a predisposing factor for developing PAMC.
• Further research is warranted to understand this association.