Primary atrial fibromyxosarcoma with multiple-system metastases: A case report
Jingping Qiu1, Lingrong Tang, Yang Han
1Department of Radiation Oncology Department of Pathology Department of Cardiac Surgery, the First Hospital, China Medical University, Shenyang, China.
Medicine
|December 17, 2017
Summary
Primary atrial fibromyxosarcoma is a rare, highly malignant cardiac tumor. This case highlights its aggressive nature and potential for widespread metastases, emphasizing the need for considering malignancy in cardiac masses.
Area of Science:
- Cardiology
- Oncology
- Pathology
Background:
- Fibromyxosarcoma typically presents with low-grade malignancy in various body sites.
- Primary atrial fibromyxosarcoma is exceptionally rare, especially with aggressive behavior.
Observation:
- A 34-year-old female presented with chest oppression, shortness of breath, and headache.
- Echocardiography revealed a left atrial mass near the mitral valve.
Findings:
- Postoperative histopathology confirmed left atrium fibromyxosarcoma.
- Metastases were identified in the adnexa, adrenal glands, iliacus, brain, and skeletal system via PET/CT scan.
Implications:
- Cardiac fibromyxosarcoma, though rare, can be a highly malignant neoplasm with systemic metastatic potential.
- Malignancy should be considered in the differential diagnosis of cardiac masses.
