Dental management of a child with familial dysautonomia

Familial dysautonomia is a hereditary sensory neuropathy that involves sensory, motor, and central components of the nervous system. Orofacial features include a tendency toward facial concavity in the child, and convexity in the adult. There is increased salivation, and crowded teeth and malocclusion are characteristic. This patient is not Jewish; this makes his case an extremely rare one.