Complete Resection of a Right-Sided Interventricular Septal Fibroma

Area of Science:

• Pediatric Cardiology
• Cardiac Oncology
• Congenital Heart Disease

Background:

• Cardiac fibromas are rare benign tumors in infants and children.
• Intracardiac masses can lead to significant hemodynamic compromise and arrhythmias.
• Early diagnosis and intervention are crucial for managing pediatric cardiac tumors.

Observation:

• A 15-month-old infant presented with a systolic cardiac murmur and developed nonsustained ventricular tachycardia.
• Transthoracic echocardiography and magnetic resonance imaging revealed a large intracardiac mass causing interventricular septum widening and right ventricular outflow tract obstruction.
• The mass was suspected to be a cardiac fibroma due to the risk of life-threatening arrhythmias.

Findings:

• Surgical resection of the intracardiac mass was performed despite its challenging location.
• Complete tumor removal was achieved successfully.
• Microscopic examination confirmed the diagnosis of ventricular fibroma.

Implications:

• This case highlights the importance of prompt diagnosis and surgical management of cardiac fibromas in infants.
• Successful resection can prevent life-threatening arrhythmias and improve cardiac function.
• Pediatric cardiac surgeons should be prepared for complex tumor resections in challenging anatomical locations.