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Management of a Rare Variant of Hypertrophic Cardiomyopathy

Sidra Khalid1, Murtaza Sundhu1, Alinda Sarma2

  • 1Internal Medicine Residency, Fairview Hospital, Cleveland Clinic, USA.

Cureus
|March 22, 2018
PubMed

Insights

Apical hypertrophic cardiomyopathy (HCM) is a rare condition. While often benign, this case highlights the need to evaluate sudden cardiac death risk in apical HCM patients.

Area of Science:

  • Cardiology
  • Cardiovascular Imaging
  • Internal Medicine

Background:

  • Apical hypertrophic cardiomyopathy (HCM) represents a rare morphologic variant of the disease.
  • Distinguishing apical HCM from other forms of left ventricular hypertrophy is crucial for accurate diagnosis and management.

Observation:

  • A 26-year-old female presented with symptoms suggestive of apical HCM.
  • Electrocardiogram revealed characteristic T-wave inversions in precordial leads (V2-V5).
  • Echocardiography demonstrated significant apical left ventricular hypertrophy.

Findings:

  • Cardiac magnetic resonance imaging (MRI) confirmed the diagnosis of apical HCM.
  • The patient was successfully treated with beta-blocker medication.
  • Apical HCM is generally considered a relatively benign condition based on this case.

Implications:

  • Despite its typically benign nature, apical HCM carries an emerging risk of sudden cardiac death.
  • Risk stratification for sudden cardiac death is essential in patients diagnosed with apical HCM.
  • Further research is warranted to fully understand and mitigate the risks associated with apical HCM.

Keywords:
apical hypertrophic cardiomyopathycardiac mrisudden cardiac death

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