Imaging findings of IgG4-related hepatopathy: A rare case presenting as a hepatic mass

IgG4-related hepatopathy is usually referred to as parenchymal involvement of IgG4-related disease of the liver. As this disease entity was only recently described, little is known of its pathogenesis or imaging findings. We report a rare case of IgG4-related hepatopathy which presented as an ill-defined heterogeneously enhancing hepatic mass with diffusion restriction and a hepatobiliary phase defect in MR and CT images. Pathologic characteristics of the disease and its imaging findings are reviewed.