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Trehalose reduces retinal degeneration, neuroinflammation and storage burden caused by a lysosomal hydrolase

Parisa Lotfi1, Dennis Y Tse2,3, Alberto Di Ronza1

  • 1a Department of Molecular and Human Genetics , Baylor College of Medicine, Jan and Dan Duncan Neurological Research Institute at Texas Children's Hospital , Houston , TX , USA.

Autophagy
|June 20, 2018
PubMed

Keywords:
Autophagic vacuolesERGMPS IIIBSanfilippo syndromeTFEBautophagylysosomal storage diseasesmucopolysaccharidosis type IIIBretinatrehalose

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