Communication outcomes following cochlear implantation in a child with cystic cochleovestibular anomaly

Cochlear implantation is one of the best amongst the various management options available for children and adults with severe to profound sensorineural hearing loss. Inner ear and internal auditory canal (IAC) malformations accounts to approximately 25% of congenital sensorineural hearing loss in children. The primary goal of this report was to evaluate the communication outcomes after cochlear implantation in a child with cystic cochleovestibular anomaly (CCVA). The child was evaluated through various standardized outcome measures at regular intervals to track the progress in terms of auditory and spoken language skills. The scores on Categories of Auditory Perception (CAP), Meaningful Auditory Integration Scale (MAIS), Speech Intelligibility Rating (SIR), Meaningful Use of Speech Scale (MUSS), and listening and spoken language skills showed a significant leap in 12 months duration post implantation. The report thus highlights and correlates the significant progress in auditory and spoken language skills of the child with congenital malformations to appropriate auditory rehabilitation and intensive parental training.