[Postmortem study of case I of the original family of Roussy and Melle Lévy]

Post-mortem examination of case I of Roussy and Lévy's original family shows an extensive Schwann cell proliferation with some onion bulb formations. This confirms that this family is suffering from a form of hypertrophic neuropathy. The author reaffirms his concept of Roussy-Lévy syndrome as an autonomous hypertrophic neuropathy. The following criteria seem to justify the autonomy of this syndrome: dominant transmission, very precocious onset, extreme slowness of the evolution, and remarkable benignity of the general prognosis.