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Updated: Feb 5, 2026

Vascular Occlusion Training for Inclusion Body Myositis: A Novel Therapeutic Approach
Published on: June 5, 2010
Terminal osseous dysplasia presenting with intracytoplasmic inclusion bodies in digital fibromas
Joao R V Gontijo1, Wandilza F Dos Santos2, Bernardo Gontijo2
1Department of Dermatology, Oregon Health and Science University, Portland, Oregon.
Abstract:
Terminal osseous dysplasia is a rare, X-linked syndrome, presumptively embryonic lethal in males, which has recently been described with highly characteristic skin findings. The presence of intracytoplasmic inclusion bodies in fibroblasts has been considered an exclusive finding of infantile digital fibromatosis. This is the first report documenting digital fibromas with intracytoplasmic inclusion bodies in a classic case of terminal osseous dysplasia.
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