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Updated: Feb 4, 2026

Standardized Technique of Aortic Valve Re-implantation for Valve-sparing Aortic Root Replacement
Published on: December 11, 2017
Maroteaux-Lamy syndrome: a rare and challenging case of mitral valve replacement
Douglas Jw Bell1, Cheng He1, John L Pauli2
11 Department of Cardiothoracic Surgery, The Prince Charles Hospital, Chermside, Australia.
Abstract:
Maroteaux-Lamy syndrome is a very rare multisystem disorder. Cardiac valve surgery is common in these patients who present a unique set of perioperative and intraoperative challenges to the surgeon and treating team. We describe successful mitral valve replacement using an inverted aortic prosthesis in a 29-year-old lady with Maroteaux-Lamy syndrome, with a good result at 10 months.
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