Malignant fibrous histiocytoma of the vulva

Malignant fibrous histiocytoma is a sarcoma that usually occurs in the extremities of elderly patients. Primary sarcomas of the vulva are extreme rarities. The most common vulvar sarcoma is leiomyosarcoma. Only two case reports on malignant fibrous histiocytoma in vulva have previously been published. It is a malignant tumor capable of metastasizing by hematogenous and lymphatic routes. The therapy of choice is radical surgery.