Vestibular findings in 25 patients with Waardenburg's syndrome

Vestibular pathology does not seem to occur more frequently in patients with Waardenburg's syndrome than in those suffering from other types of congenital deafness. This was concluded from the results of vestibular examination by means of electronystagmography of 25 subjects with Waardenburg's syndrome from five families in the Netherlands. Ten of these subjects had a hearing loss, four of them bilateral and six unilateral. A review of the literature concerning more than 1,000 cases with Waardenburg's syndrome shows that in only 26 deaf patients was a very simple vestibular examination performed (in only three patients by means of electronystagmography).