Sinonasal Myxoma: A Distinct Lesion of Infants

Parth Mewar1, Karen E González-Torres2, T Matthew Jacks3

  • 1Head and Neck Pathology, Joint Pathology Center, 606 Stephen Sitter Ave., Silver Spring, MD, 20910-1290, USA. parth.mewar.mil@mail.mil.

Head and Neck Pathology
|November 29, 2018
PubMed

Insights

A rare sinonasal myxoma was diagnosed in an 11-month-old infant presenting with facial swelling. Complete surgical resection was successful, highlighting key diagnostic features for this pediatric tumor.

Area of Science:

  • Pediatric Oncology
  • Oral and Maxillofacial Surgery
  • Head and Neck Pathology

Background:

  • Sinonasal myxomas are rare benign tumors typically affecting adults.
  • Infantile presentation is exceptionally uncommon, posing diagnostic challenges.

Observation:

  • An 11-month-old male presented with right-sided nasal and buccal swelling.
  • Radiography showed a well-defined, hypodense soft tissue mass in the anterior maxilla.

Findings:

  • Histopathological and immunohistochemical analyses confirmed a sinonasal myxoma.
  • The lesion was completely excised using a combined extraoral and intraoral approach without complications.

Implications:

  • This case expands the known age spectrum for sinonasal myxoma.
  • Highlights the importance of considering rare diagnoses in pediatric head and neck masses.
  • Emphasizes the utility of multimodal diagnostic approaches in pediatric oncology.

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