Bipartite craniopharyngeal canal with a lipoma and cephalocele: a previously unreported entity

S Vinayagamani1, Bejoy Thomas2, Jaypalsinh Gohil3

  • 1Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Room no 318, Srishty building, SCTIMST Staff Quarters, Poondi Road, Kumarapuram Junction, Medical college (P.O), Trivandrum, Kerala, 695011, India. dr.vinayagamani@gmail.com.

Acta Neurochirurgica
|January 15, 2019
PubMed

Insights

This study reports a rare case of a bipartite craniopharyngeal canal with lipoma and cephalocele in a child, a previously undocumented anatomical variation. Understanding this finding is crucial for potential surgical interventions.

Area of Science:

  • Neuroimaging
  • Pediatric Neurology
  • Craniofacial Anatomy

Background:

  • Craniopharyngeal canal anatomy and its variations.
  • Embryological development of the skull base.
  • Surgical considerations in pediatric neurosurgery.

Observation:

  • A 13-year-old male presented with headache and declining vision.
  • MRI revealed a large, bipartite craniopharyngeal canal with a bony septum.
  • Associated findings included a lipoma and cephalocele on either side of the septum.

Findings:

  • First reported case of a bipartite craniopharyngeal canal with associated lipoma and cephalocele.
  • The child exhibited normal pituitary function despite nonvisualization of the pituitary gland on MRI.
  • Discussion of potential embryological origins for this rare anatomical variant.

Implications:

  • Highlights the importance of recognizing rare anatomical variations in the skull base.
  • May influence surgical approaches in cases involving the craniopharyngeal canal.
  • Contributes to the understanding of craniofacial development and associated anomalies.