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"Switched" metabolic acidosis in mitochondrial diabetes mellitus
Yamato Keidai1, Yorihiro Iwasaki1, Sachiko Honjo1
1Center for Diabetes and Endocrinology, The Tazuke Kofukai Medical Research Institute Kitano Hospital, Osaka, Japan.
Journal of Diabetes Investigation
|January 20, 2019
Abstract:
A patient with mitochondrial diabetes mellitus developed diabetic ketoacidosis. During insulin treatment, although diabetic ketoacidosis improved, lactic acidosis unexpectedly worsened. This clinical course, named "switched metabolic acidosis," could reflect the unique pathophysiology of the mitochondrial disorder.