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Immunoglobulin G4 Inflammatory Aortic Aneurysm Mimicking Acute Aortic Syndrome
Robert Blazekovic1, Mislav Planinc2, Jasmina Catic3
1Department of Cardiac and Transplant Surgery, Dubrava University Hospital, Zagreb, Croatia; Faculty of Medicine, "J.J. Strossmayer" University of Osijek, Osijek, Croatia.
Abstract:
Immunoglobulin-G4-related disease (IgG4RD) is a novel clinical entity characterized by lymphoplasmacytic infiltrates presenting as an excessive fibrosis such as retroperitoneal inflammatory pseudotumor but rarely affecting the heart or the aorta. We describe a case of IgG4RD with multifocal aortic involvement presenting as an acute aortic syndrome.
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