Neurofibromatosis

Since first so named in 1882, von Recklinghausen's disease has been reported to have a wide variety of associated defects, including the more common intracranial and extracranial neuromas and the less common intracerebral tumors and large artery ectasias, aneurysms, and spontaneous fistulas, in addition to a variety of small vessel tumors and arteriovenous fistulas. A case is reported with the association of a vertebral artery spontaneous fistula along with spontaneous spinal fluid rhinorrhea and a Chiari type I malformation. Review of the literature reveals no report of either of the latter two associated with von Recklinghausen's disease.