Visual Loss Post Ross Procedure in an Adolescent With Newly Diagnosed Mucopolysaccharidosis Type II

Perioperative visual loss is a rare but serious complication after cardiac surgery. The etiology is not fully understood, and there is no consensus on the optimal management of this condition. A 15-year-old male patient developed severe visual impairment attributed to nonarteritic anterior ischemic optic neuropathy after a Ross aortic root replacement procedure. A new diagnosis of the lysosomal storage disorder, mucopolysaccharidosis type II (Hunter syndrome), was subsequently made, raising questions about the pathogenesis of this devastating postoperative complication.