Congenital anomaly of coronary artery: absence of left circumflex artery
Muhammad Shabbir Rawala1, Amna Saleem Ahmed2, Muhammad Asif Iqbal3
1Department of Internal Medicine, WVU-Charleston Division, Charleston, WV, USA.
Insights
Congenital coronary artery anomalies affect 1% of people and can cause sudden death. This case highlights how artery variations impact cardiac interventions for chest pain.
Area of Science:
- Cardiology
- Anatomical Pathology
Background:
- Congenital coronary artery anomalies occur in approximately 1% of the population.
- These anomalies are a significant cause of sudden cardiac death in younger individuals.
- Congenital absence of the left circumflex artery is typically benign but can manifest as exertional angina.
Observation:
- A 59-year-old female presented with chest pain, prompting cardiology evaluation.
- Invasive coronary angiography was performed to assess coronary anatomy.
- The angiogram revealed the absence of the left circumflex artery.
Findings:
- A large right coronary artery was noted.
- Prominent septal and diagonal branches originating from the left main coronary artery were observed.
- These findings suggest a potential compensatory mechanism to perfuse territories normally supplied by the absent left circumflex artery.
Implications:
- Accurate definition of coronary anatomy is crucial for managing patients with coronary artery anomalies.
- Understanding anomalous coronary anatomy guides the selection of appropriate cardiac interventions in cases of myocardial ischemia.
- This case underscores the importance of detailed angiographic assessment in patients presenting with cardiac symptoms and suspected coronary anomalies.
Abstract:
The prevalence of congenital coronary artery anomalies is approximately 1% in the general population. They are a common cause of sudden death in younger persons. Congenital absence of the left circumflex artery is usually a benign condition but can cause symptoms of exertional angina. We present a case of a 59-year-old female who presented with complaints of chest pain. She was evaluated by the cardiology service. An invasive angiogram identified the absence of the circumflex artery, a large right coronary artery, and large septal and diagonal branches of the left main coronary artery possibly as a compensatory mechanism to supply blood to the LCx territories. It is important to define coronary anatomy as anomalies dictate which cardiac intervention should be attempted in cases of ischemia.
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