A Successful Repair of Pseudocoarctation With Associated Aortic Arch Aneurysm in an Eight-Month-Old Infant

Roman Sekelyk1, Zufar Abdurakhmanov1, Andrii Kurkevych2

  • 1Department of Cardiac Surgery of Newborns and Early Childhood, Ukrainian Children's Cardiac Center, Kyiv, Ukraine.

Insights

This study presents a rare case of pseudocoarctation of the aorta in an infant, successfully treated with surgical aortic arch reconstruction. The procedure avoided prosthetic use, ensuring a favorable outcome.

Area of Science:

  • Cardiovascular Surgery
  • Pediatric Cardiology
  • Medical Imaging

Background:

  • Pseudocoarctation of the aorta is a rare congenital anomaly.
  • Characterized by aortic arch elongation and tortuosity, often associated with aneurysms.

Purpose of the Study:

  • To report a successful surgical management of pseudocoarctation of the aorta in a pediatric patient.
  • To highlight the use of advanced imaging and a prosthesis-free reconstruction technique.

Main Methods:

  • Prenatal diagnosis using magnetic resonance imaging.
  • Postnatal confirmation with computed tomography angiography.
  • Surgical resection of the aneurysmal aorta with extended end-to-end reconstruction and left subclavian artery reimplantation.

Main Results:

  • The infant underwent successful aortic arch reconstruction without prosthetic material.
  • Postoperative imaging confirmed no residual stenosis at six months.
  • The patient experienced an uneventful recovery.

Conclusions:

  • Surgical repair of pseudocoarctation of the aorta is feasible and effective in infants.
  • Prosthesis-free reconstruction is a viable option for managing this condition.
  • Early diagnosis and timely intervention are crucial for optimal outcomes.

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