Pleural-Based Intrathoracic Cystic Lymphangioma in an Infant Mimicking a Pneumonia

Zev Frimer1, Daniel Fink2, Ruth Cytter-Kuint3

  • 1Pediatric Pulmonary Unit, Shaare Zedek Medical Center, Affiliated to the Hebrew University, School of Medicine, Jerusalem, Israel.

Insights

This study details the first infant case of a pleural-based cystic lymphangioma, a rare benign tumor. Complete surgical removal was successful, with no recurrence observed a year later.

Area of Science:

  • Pediatric Surgery
  • Thoracic Oncology
  • Medical Imaging

Background:

  • Cystic lymphangioma is a rare benign tumor typically found in the neck of children.
  • Pleural-based cystic lymphangioma is exceptionally uncommon, especially in infants.

Observation:

  • An infant presented with right upper lobe pneumonia.
  • Persistent radiographic findings prompted CT and MRI scans.
  • Imaging revealed a multiloculated cystic lesion in the right hemithorax.

Findings:

  • Histopathological examination confirmed a pleural-based intrathoracic cystic lymphangioma.
  • Complete surgical resection of the tumor was achieved.
  • The infant experienced a full recovery with no signs of recurrence one year post-surgery.

Implications:

  • This case expands the known locations for cystic lymphangioma.
  • Early diagnosis and surgical intervention are crucial for favorable outcomes.
  • Highlights the importance of advanced imaging in diagnosing intrathoracic lesions.

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