[Cranio-orbital neurofibromatosis. Apropos of a case]

Principal general manifestations of Recklinghausen's disease are outlined, with emphasis on cephalic lesions, particularly cranio-orbital localizations responsible in a large number of cases for lysis of greater wing of sphenoid. This is associated, amongst other complications, with ophthalmologic sequelae. A clinical case is presented, allowing discussion of the two essential problems raised by cranio-orbital neurofibromatosis: 1) conservation or not of the eye during necessary surgical treatment and 2) the course of the disease which is always progressive.