Surgical Repair of Complete Congenital Sternal Cleft Associated With Pectus Excavatum

Alexander E P Smith1, Aleksander Mani1, Andrew Jones1

  • 1Department of Thoracic Surgery, Royal Brompton Hospital NHS Foundation Trust, London, United Kingdom.

Insights

This case report details the surgical repair of a rare congenital cleft sternum and pectus excavatum in a 13-year-old girl. The modified Ravitch procedure successfully corrected the defect, highlighting the importance of preoperative imaging.

Area of Science:

  • Congenital thoracic anomalies
  • Pediatric surgery
  • Cardiothoracic surgery

Background:

  • Complete congenital cleft sternum is a rare condition.
  • It is often associated with pectus excavatum, creating complex surgical challenges.
  • Current surgical standards are primarily based on case reports and series.

Observation:

  • A 13-year-old girl presented with a complete congenital cleft sternum and anterior pericardial defect, along with pectus excavatum.
  • Surgical intervention was necessary to address these significant thoracic abnormalities.
  • Preoperative imaging played a crucial role in accurately defining the extent of the defect.

Findings:

  • A modified Ravitch procedure was employed for the surgical repair.
  • The cleft sternum and pectus excavatum were corrected using stainless steel wires for defect closure.
  • A pectus bar was inserted to provide structural support.

Implications:

  • This case demonstrates a successful surgical approach for a complex congenital sternal defect.
  • The modified Ravitch procedure offers a viable option for repairing cleft sternum and pectus excavatum.
  • Emphasizes the critical role of detailed preoperative imaging in planning surgical repair for such rare anomalies.

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