Surgical Repair of Complete Congenital Sternal Cleft Associated With Pectus Excavatum
Alexander E P Smith1, Aleksander Mani1, Andrew Jones1
1Department of Thoracic Surgery, Royal Brompton Hospital NHS Foundation Trust, London, United Kingdom.
Insights
This case report details the surgical repair of a rare congenital cleft sternum and pectus excavatum in a 13-year-old girl. The modified Ravitch procedure successfully corrected the defect, highlighting the importance of preoperative imaging.
Area of Science:
- Congenital thoracic anomalies
- Pediatric surgery
- Cardiothoracic surgery
Background:
- Complete congenital cleft sternum is a rare condition.
- It is often associated with pectus excavatum, creating complex surgical challenges.
- Current surgical standards are primarily based on case reports and series.
Observation:
- A 13-year-old girl presented with a complete congenital cleft sternum and anterior pericardial defect, along with pectus excavatum.
- Surgical intervention was necessary to address these significant thoracic abnormalities.
- Preoperative imaging played a crucial role in accurately defining the extent of the defect.
Findings:
- A modified Ravitch procedure was employed for the surgical repair.
- The cleft sternum and pectus excavatum were corrected using stainless steel wires for defect closure.
- A pectus bar was inserted to provide structural support.
Implications:
- This case demonstrates a successful surgical approach for a complex congenital sternal defect.
- The modified Ravitch procedure offers a viable option for repairing cleft sternum and pectus excavatum.
- Emphasizes the critical role of detailed preoperative imaging in planning surgical repair for such rare anomalies.
Abstract:
Complete congenital cleft sternum associated with pectus excavatum is a rare abnormality. Case reports and case series currently provide the technical standards for comparison in surgical repair. We present a case report of surgical repair of cleft sternum and anterior pericardial defect associated with pectus excavatum in a 13-year-old girl. The surgical repair of the cleft sternum and pectus excavatum was performed with a modified Ravitch procedure, closure of the defect with stainless steel wires, and insertion of a pectus bar. Preoperative imaging is important in better defining the defect.
Related Concept Videos
Mismatch Repair
Mismatch Repair
The Mutator Protein Family Plays a Key Role in DNA Mismatch Repair
The human genome has more than 3 billion base pairs of DNA per cell. Prior to cell division, that vast amount of genetic...
Nucleotide Excision Repair
Nucleotide Excision Repair
Cells are regularly exposed to mutagens—factors in the environment that can damage DNA and generate mutations. UV radiation is one of the most common mutagens and is estimated to introduce a significant number of changes in DNA. These include bends or kinks in the structure, which can block DNA replication or transcription. If these errors are not fixed, the damage can cause mutations, which in turn can result in cancer or disease depending on which sequences are...
Overview of DNA Repair
Chemically...
Base Excision Repair
The first step of...


