Safety and efficacy of intravenous Colchicine in children with Familial Mediterranean Fever

Rotem Tal1,2, Rotem Semo Oz1, Gil Amarilyo3,4

  • 1Pediatric Day Care Center, Schneider Children's Medical Center of Israel, 4920235, Petach Tikva, Israel.

Insights

Intravenous (IV) Colchicine is safe and effective for pediatric Familial Mediterranean Fever (FMF) patients unresponsive to oral Colchicine. This treatment improved health and reduced attacks, offering a valuable option where biologics are unavailable.

Area of Science:

  • Pediatric Rheumatology
  • Genetics and Genomics
  • Pharmacology

Background:

  • Familial Mediterranean Fever (FMF) is a common monogenic inflammatory disease.
  • Oral Colchicine is the primary treatment, but 5% of patients are non-responders.
  • Intravenous (IV) Colchicine has demonstrated efficacy and safety in adult FMF patients.

Purpose of the Study:

  • To evaluate the safety and efficacy of IV Colchicine in pediatric FMF patients.
  • To assess outcomes in children refractory to maximal oral Colchicine doses.
  • To establish a safety profile for prolonged IV Colchicine use in pediatric FMF.

Main Methods:

  • Retrospective review of medical records for pediatric FMF patients treated with IV Colchicine.
  • Inclusion criteria: FMF diagnosis, <18 years at IV Colchicine initiation, ≥6 months of therapy.
  • Data collected included laboratory results, treatment duration, and patient-reported outcomes via questionnaires.

Main Results:

  • Seven pediatric FMF patients (homozygous for M694V genotype) received weekly IV Colchicine.
  • 38 cumulative patient-years of follow-up showed normal laboratory results and no toxicity.
  • Significant improvements observed in global health assessment and disease-free days (P<0.05).

Conclusions:

  • Prolonged IV Colchicine use demonstrates an excellent safety profile in pediatric FMF patients.
  • IV Colchicine effectively reduces the intensity and frequency of FMF attacks.
  • It serves as a viable second-line therapy where anti-interleukin 1 blockers are inaccessible or as a third-line option after biologic failure.

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