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Published on: August 28, 2018
Anomalous Coronary Anatomy with Fistula Diagnosed on Coronary Computed Tomography Angiography
Khurram Butt1, Ali Agha2, Ryan Parente3
1Internal Medicine, Florida Hospital, Orlando, USA.
Insights
This study highlights two rare cases of anomalous coronary arteries in children. Early identification and intervention are crucial for preventing severe cardiac events and sudden cardiac death.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiovascular Imaging
Background:
- Anomalous coronary vasculature is uncommon but can lead to serious adverse events, including sudden cardiac death.
- Accurate diagnosis of aberrant coronary anatomy is vital for appropriate patient management.
- This report details two pediatric cases with distinct congenital coronary anomalies.
Observation:
- Case 1: A 4-year-old male presented with chest pain, revealing anomalous left coronary artery origin from the right sinus with a malignant interarterial course and myocardial bridging.
- Case 2: A neonate with hypoplastic right ventricle and pulmonary atresia exhibited a coronary sinus fistula and atrial appendage bridge.
Findings:
- Coronary computed tomography angiography (CCTA) precisely delineated the complex coronary anatomy in both cases.
- Surgical correction was successful for the patient in Case 1.
- The infant in Case 2 required transfer for cardiac transplantation due to the complexity of the anomalies.
Implications:
- These cases underscore the importance of advanced imaging techniques like CCTA in diagnosing rare coronary anomalies.
- Timely surgical intervention or advanced therapies can improve outcomes in pediatric patients with aberrant coronary arteries.
- Understanding these rare variations is essential for pediatric cardiac care and research.
Abstract:
Anomalous coronary vasculature is a rare finding among the general population. Identifying such cases is important for preventing adverse outcomes such as sudden cardiac death. We present two rare cases of aberrant coronary anatomy. In Case 1, a 4-year-old male who presented with non-exertional chest pain was found to have anomalous coronary architecture on echocardiogram. Coronary computed tomography angiogram (CCTA) confirmed an anomalous origin of the left coronary artery from the right coronary sinus with a malignant interarterial course and myocardial bridging of the left anterior descending (LAD) artery. The patient underwent a successful surgical correction of the defects. In Case 2, a full-term infant female was born with a hypoplastic right ventricle and pulmonary atresia. CCTA showed a large fistula originating from the coronary sinus on the left that drained into the superior aspect of the mid right ventricular cavity, an anomalous bridge between the left and right atrial appendages, and five fistulous connections between various vessels. The patient was transferred to another facility for cardiac transplant.
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