Anomalous Coronary Anatomy with Fistula Diagnosed on Coronary Computed Tomography Angiography

Khurram Butt1, Ali Agha2, Ryan Parente3

  • 1Internal Medicine, Florida Hospital, Orlando, USA.

Cureus
|June 28, 2019
PubMed

Insights

This study highlights two rare cases of anomalous coronary arteries in children. Early identification and intervention are crucial for preventing severe cardiac events and sudden cardiac death.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Cardiovascular Imaging

Background:

  • Anomalous coronary vasculature is uncommon but can lead to serious adverse events, including sudden cardiac death.
  • Accurate diagnosis of aberrant coronary anatomy is vital for appropriate patient management.
  • This report details two pediatric cases with distinct congenital coronary anomalies.

Observation:

  • Case 1: A 4-year-old male presented with chest pain, revealing anomalous left coronary artery origin from the right sinus with a malignant interarterial course and myocardial bridging.
  • Case 2: A neonate with hypoplastic right ventricle and pulmonary atresia exhibited a coronary sinus fistula and atrial appendage bridge.

Findings:

  • Coronary computed tomography angiography (CCTA) precisely delineated the complex coronary anatomy in both cases.
  • Surgical correction was successful for the patient in Case 1.
  • The infant in Case 2 required transfer for cardiac transplantation due to the complexity of the anomalies.

Implications:

  • These cases underscore the importance of advanced imaging techniques like CCTA in diagnosing rare coronary anomalies.
  • Timely surgical intervention or advanced therapies can improve outcomes in pediatric patients with aberrant coronary arteries.
  • Understanding these rare variations is essential for pediatric cardiac care and research.

Related Concept Videos

Coronary Circulation01:21

Coronary Circulation

The heart, an organ critical to survival, gets nourishment not from the blood it pumps but from a separate circulation system known as coronary circulation. This is the shortest circulation in the body and is responsible for supplying the heart with the nutrients it needs to function effectively.
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
6.8K
Computed Tomography01:10

Computed Tomography

Tomography refers to imaging by sections. Computed tomography (CT) is a non-invasive imaging technique that uses computers to analyze several cross-sectional X-rays to reveal minute details about structures in the body.
The technique was invented in the 1970s and is based on the principle that as X-rays pass through the body, they are absorbed or reflected at different levels. In the technique, a patient lies on a motorized platform while a computerized axial tomography (CAT) scanner rotates...
8.1K
Coronary Artery Disease I: Introduction01:30

Coronary Artery Disease I: Introduction

Coronary Artery Disease (CAD): An Overview with Scientific InsightsCoronary Artery Disease (CAD), often referred to as C-A-D, is a prevalent blood vessel disorder classified under the broader category of atherosclerosis. Atherosclerosis is a pathological process characterized by the hardening and narrowing of arteries due to the accumulation of atherosclerotic plaques. These plaques are composed of cholesterol, fatty substances, inflammatory cells, calcium, and fibrin, reducing blood flow to...
912
Coronary Artery Disease II: Pathophysiology01:26

Coronary Artery Disease II: Pathophysiology

Coronary Artery Disease (CAD) originates from a series of events that impair the function of coronary arteries, the blood vessels responsible for delivering oxygen-rich blood to the heart muscle. The pathophysiology of CAD is closely linked to atherosclerosis, a chronic inflammatory and lipid-driven condition affecting the vascular endothelium.1. Endothelial DamageThe process begins with damage to the vascular endothelium, which serves as a protective barrier between the blood and the vessel...
390
Acute Coronary Syndrome I: Introduction01:30

Acute Coronary Syndrome I: Introduction

Acute Coronary Syndrome (ACS) encompasses a spectrum of heart conditions caused by sudden obstruction of coronary arteries, typically resulting from the rupture of an atherosclerotic plaque and subsequent thrombus (blood clot) formation. This obstruction can lead to partial or complete blockage of blood flow, causing varying degrees of myocardial ischemia or infarction.ACS includes the following clinical entities:Unstable Angina (UA)Non-ST-Elevation Myocardial Infarction (NSTEMI)ST-Elevation...
877
Anatomy of the Circulatory System02:03

Anatomy of the Circulatory System

The human circulatory system consists of blood, blood vessels that carry blood away from the heart, around the body, and back to the heart, and the heart itself, which acts as a central pump. The systemic circuit supplies blood to the whole body, the coronary circuit supplies blood to the heart, and the pulmonary circuit supplies blood flow between the heart and lungs.
97.8K