Perforated mucocele of the appendix in the left upper quadrant: A challenging anatomy and an improvised surgical

Basmah Faris Alhassan1, Abdullah Saji Alharbi2, Walid Mokhtar Omar1

  • 1Department of General Surgery, King Khalid University Hospital and College of Medicine, King Saud University, Saudi Arabia.

Abstract

Insights

Pseudomyxoma peritonei (PMP) with intestinal malrotation presents unique surgical challenges. Cytoreductive surgery (CRS) and heated intraperitoneal chemotherapy (HIPEC) offer a safe and effective treatment, even with an improvised technique for colon preservation.

Area of Science:

  • Surgical Oncology
  • Gastrointestinal Surgery

Background:

  • Pseudomyxoma peritonei (PMP) is a rare but serious complication of appendicular mucocele perforation.
  • Intestinal malrotation in adults is often asymptomatic but can complicate presentations of other conditions, delaying diagnosis.
  • The co-occurrence of PMP and intestinal malrotation is exceptionally rare, posing significant clinical and diagnostic challenges.

Purpose of the Study:

  • To present a case of PMP in a patient with co-existing intestinal malrotation.
  • To describe the management of this rare condition using cytoreductive surgery (CRS) and heated intraperitoneal chemotherapy (HIPEC).

Main Methods:

  • A case report detailing the surgical management of PMP in a patient with intestinal malrotation.
  • Application of CRS and HIPEC with an improvised surgical technique for colon preservation due to anatomical abnormalities.

Main Results:

  • The patient was successfully managed with CRS and HIPEC.
  • An improvised surgical technique allowed for safe and effective preservation of part of the colon, overcoming intraoperative challenges posed by extensive disease and abnormal anatomy.

Conclusions:

  • CRS/HIPEC is an effective treatment for PMP, improving patient outcomes.
  • This case highlights the importance of early recognition of uncommon surgical conditions.
  • The described improvised surgical technique is safe and effective for preserving colon segments in selected PMP patients with intestinal malrotation.

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