Atypical cutaneous and histological presentation of adult-onset Still's disease

Adult-onset Still's disease (AOSD), the adult variant of systemic juvenile idiopathic arthritis, is a rare auto-inflammatory condition that presents with characteristic skin findings. There is no specific test available; diagnosis is usually based on the symptoms and evanescent rash found in patients. More recently, however, descriptions of atypical cutaneous and histological manifestations of AOSD have been published. We describe a case of atypical AOSD and discuss recent literature on this different cutaneous and histological presentation. Our results add to the growing discussion on atypical AOSD and suggest that this presentation may have been underreported and more common than previously thought.