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Left ventricular non-compaction in a patient with Shone's complex
Mehrnoush Toufan1, Lelll Pourafkari1, Aldln Baghbani-Oskouel2
1Department of Cardiology, Cardiovascular Research Center, Tabriz University of Medical Sciences, Tabriz, Iran.
Insights
Shone's complex, a rare congenital heart defect with multiple left-sided obstructions, was unusually found in an adult with left ventricular non-compaction cardiomyopathy (NCC). This previously undescribed association highlights a new diagnostic consideration for complex cardiac conditions.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiomyopathy
Background:
- Shone's complex involves multiple obstructive lesions in the left heart.
- Congenital cardiac malformations require ongoing research for diagnosis and treatment.
Observation:
- An adult male presented with palpitations and dyspnea.
- Echocardiography identified Shone's complex.
Findings:
- The patient was diagnosed with Shone's complex.
- Left ventricular non-compaction cardiomyopathy (NCC) was also identified.
- This co-occurrence of Shone's complex and NCC is novel.
Implications:
- This case expands the understanding of Shone's complex presentations.
- It suggests NCC should be considered in adults with Shone's complex.
- Further research is needed to explore this association and its clinical significance.
Abstract:
Shone's complex is a rare congenital cardiac malformation characterized by serial obstructive lesions of the left heart at multiple levels. Presently described is an unusual case of an adult male patient who presented with palpitations and worsening dyspnea. An echocardiographic evaluation revealed Shone's complex associated with left ventricular non-compaction cardiomyopathy (NCC). To our knowledge, an association between NCC and Shone's complex has not been previously described.
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