Aesthetic Cranial Vault Expansion in a Child With Slit Ventricle Syndrome and Eumorphic Face

Gabriele Canzi1, Anna Maria Auricchio2, Giorgia Iacopino3

  • 1Maxillofacial Operative Unit, the Emergency Department, ASST Grande Ospedale Metropolitano Niguarda, Milan.

Insights

Slit ventricle syndrome (SVS) and secondary craniosynostosis (SCS) in children can be treated with innovative post-coronal vault expansion. This surgical approach increases cranial volume while preserving facial structure.

Area of Science:

  • Neurosurgery
  • Pediatric Neurosurgery
  • Craniofacial Surgery

Background:

  • Hydrocephalus is commonly treated with ventricular shunting.
  • Slit ventricle syndrome (SVS) with craniocerebral disproportion (CCD) and secondary craniosynostosis (SCS) are rare complications of CSF shunting in children.
  • Current management for SVS/SCS includes shunt revision, anti-siphon devices, or endoscopic third ventriculostomy, with cranial expansion reserved for refractory cases.

Observation:

  • Anterior cranial vault expansion, a common surgical approach for SVS/SCS, can lead to significant facial disproportions.
  • A 6-year-old boy presented with SVS and SCS, maintaining normal facial features.
  • The patient underwent an innovative post-coronal vault expansion procedure.

Findings:

  • The novel post-coronal vault expansion successfully increased intracranial volume.
  • This technique avoided iatrogenic alterations in facial proportions.
  • The patient experienced a favorable outcome without changes to facial conformation.

Implications:

  • Post-coronal vault expansion offers a promising alternative for managing SVS/SCS in pediatric patients.
  • This approach may reduce the need for further shunt revisions and improve neurological symptoms.
  • It presents a method to achieve cranial volume expansion while preserving facial aesthetics in pediatric neurosurgery.

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