Aortopulmonary Window With Pulmonary Atresia and Interrupted Aortic Arch: A Very Rare Triad
Doaa A Shahbah1, Nicole L Herrick1,2, Howaida El-Said2
1Rady Children's Hospital, San Diego, CA, USA.
Abstract:
Aortopulmonary window (APW) is a rare lesion, accounting for 0.2% to 0.6% of all congenital heart diseases. We report a rare case of an infant with APW, interrupted aortic arch, and pulmonary atresia with intact interventricular septum and right ventricle-dependent coronary circulation. This report describes the anatomy of this lesion set, the complex surgical palliation that was required, and the management of postoperative complications.
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