Primary Angiosarcoma of Parotid Gland in a Child: A Rare Case with Diagnostic Challenge

Primary angiosarcoma of salivary glands is a rare entity that most commonly arises in the parotid gland and affects adults and the elderly. Angiosarcoma of the parotid gland in a child is exceedingly rare and thus can be a diagnostic challenge. We present a case of angiosarcoma of the parotid gland in a 6-year-old female child with bilateral lung metastases. The patient underwent chemotherapy and showed a partial response. Awareness of this entity in salivary glands is important for accurate and early diagnosis due to its distinct therapeutic and prognostic implications.