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Quadricuspid Aortic Valve: A Rare and Incidental Finding
Mandeep Kaur1, Htoo Kyaw2, Cesar Ayala-Rodriguez3
1Internal Medicine, Brooklyn Hospital Center, Brooklyn, USA.
Quadricuspid aortic valve (QAV), a rare congenital heart defect, was diagnosed in a pregnant patient. This case highlights the importance of monitoring for QAV during pregnancy due to potential risks.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Maternal-Fetal Medicine
Background:
- Quadricuspid aortic valve (QAV) is an extremely rare congenital heart anomaly, with limited documented cases.
- Pregnancy-associated QAV has not been previously reported in medical literature.
Observation:
- A 29-year-old pregnant patient presented with new-onset palpitations at 37 weeks gestation.
- Transthoracic echocardiography revealed a quadricuspid aortic valve (type b classification) with mild aortic regurgitation.
- The patient had no other congenital heart anomalies.
Findings:
- The patient successfully underwent a normal vaginal delivery without peripartum cardiac complications.
- This case represents the first reported instance of QAV identified during pregnancy.
Implications:
- QAV, though rare, can be associated with aortopathies, posing a high-risk state during pregnancy.
- Close cardiac monitoring is crucial for pregnant individuals with QAV, particularly in the second and third trimesters.
- Further research is needed to define the natural history and long-term outcomes of QAV, especially in pregnant populations.
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Heart Valves
The AV valves prevent the backflow of blood from the ventricles to the atria during ventricular contraction. These valves function with the assistance of the chordae tendineae and papillary muscles. When the ventricles are relaxed, the chordae tendineae are slack, allowing blood to flow from the atria into the...

