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Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis
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Adult Care in Cystic Fibrosis

J Stuart Elborn1,2

  • 1Centre for Experimental Medicine, Queen's University, Belfast, Northern Ireland, United Kingdom.

Seminars in Respiratory and Critical Care Medicine
|December 31, 2019
PubMed

Insights

Cystic fibrosis (CF) care is shifting to adults, necessitating new strategies. Adapting healthcare systems and multidisciplinary teams is crucial for improving adult CF patient quality of life and survival.

Area of Science:

  • Pulmonology and Adult Medicine
  • Healthcare Systems Research

Background:

  • Cystic fibrosis (CF) prevalence is increasing in adults, particularly in developed nations.
  • Adults now represent the majority of the CF population, with most morbidity and mortality occurring in this age group.
  • Emerging CFTR modulator therapies may further increase adult lifespan and complexity of care.

Purpose of the Study:

  • To highlight the evolving demographic of cystic fibrosis towards an adult-predominant population.
  • To emphasize the critical need for adapting healthcare models to meet the complex needs of adult CF patients.
  • To underscore the importance of multidisciplinary care and quality of life for aging adults with CF.

Main Methods:

  • This is a conceptual and review-based abstract, not detailing specific experimental methods.
  • Analysis of current trends in CF demographics and healthcare delivery.
  • Synthesis of expert opinion on future care requirements for adult CF patients.

Main Results:

  • Adults are increasingly the primary demographic for cystic fibrosis care.
  • Existing healthcare models require significant adaptation to manage the growing adult CF population.
  • Adult CF patients face complex co-morbidities, including age-related diseases, alongside CF.

Conclusions:

  • Maintaining quality of life and maximizing survival are paramount for adults with CF.
  • Adaptable, multidisciplinary teams are essential, integrating diverse specialties beyond lung health.
  • New healthcare delivery models are urgently needed to address the complex, aging adult CF population.

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