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Pulmonary lymphangioleiomyomatosis: a case report
Ling Wu1, Zhou Wang2, Yongyong Wu3
1Department of Pathology, Tongde Hospital of Zhejiang Province Hangzhou, Zhejiang, P. R. China.
International Journal of Clinical and Experimental Pathology
|January 15, 2020
Summary
Pulmonary lymphangioleiomyomatosis (PLAM) is a rare lung disease causing progressive destruction. Current treatments focus on supportive care and anti-estrogen therapy, as effective cures remain elusive for this rare tumor.
Area of Science:
- Pulmonology
- Oncology
- Rare Diseases
Background:
- Pulmonary lymphangioleiomyomatosis (PLAM) is an exceedingly rare neoplastic proliferation.
- It is characterized by diffuse, progressive destruction of the pulmonary parenchyma.
- The incidence of PLAM is less than 1 per million, highlighting its rarity.
